thalasemia

Case thalassemia

Pt hv u/l  beta thalassemia diagnosed in 2000 with hypersplenism

Currently pw lethargic, reduced effort tolerance, mild sob, dizziness, bilateral leg swelling, periorbitsl sweling

On examination ptn jaundice, pale , thalassemic facies, frontal bossing, distended abdomen, with hepatosplenomegaly( massive splenomegaly), leuconychia, elevated jvp, PSM at mitral area, (TR with loud P2)

Impression:

1.hbe beta thalasemia

2. heart failure

Ix=

pt/aptt, inr, fbc, rft, urine feme, ecg

mx-

·         -transfuse 1 pint pack cell

·         -for echo

·         -t.hematinic